@article{article343d94ac, title = {NEDD4-family E3 ligase dysfunction due to PKHD1/Pkhd1 defects suggests a mechanistic model for ARPKD pathobiology}, author = {Kaimori, Jun-ya and Lin, Cheng-Chao and Outeda, Patricia and Garcia-Gonzalez, Miguel A. and Menezes, Luis F. and Hartung, Erum A. and Li, Ao and Wu, Guanqing and Fujita, Hideaki and Sato, Yasunori and Nakanuma, Yasuni and Yamamoto, Satoko and Ichimaru, Naotsugu and Takahara, Shiro and Isaka, Yoshitaka and Watnick, Terry and Onuchic, Luiz F. and Guay-Woodford, Lisa M. and Germino, Gregory G.}, year = {2017}, doi = {10.1038/s41598-017-08284-4}, journal = {Scientific Reports} }